Sulafa KM Ali1 Author
Subjects of specialization
Affiliation
Noncompaction cardiomyopathy, Mitral regurgitation, Echocardiography
Department of Pediatric Cardiology, Sudan Heart Center, University of Khartoum, Sudan
Sulafa KM Ali Department of Pediatric Cardiology, Sudan Heart Center, University of Khartoum, Sudan. His publications include: 1. Dusek J, Ostadal B, Duskova M (1975) Postnatal persistence of spongy myocardium with embryonic blood supply. Arch Pathol 6: 312-317. 2. Engberding R, Bender F (1984) Identification of a rare congenital anomaly of the myocardium by two-dimensional echocardiography: persistence of isolated myocardial sinusoids. Am J Cardiol 11: 1733-1734.
Research Article Open Access
Author(s): Sulafa KM Ali1* and Laila M Elmahdi1*
Background: Noncompaction Cardiomyopathy (NCCM) is a primary genetic cardiomyopathy with variable clinical and Echocardiographic (echo) features. Association with Mitral Regurgitation (MR) was reported but the mechanism of this association has not been well described in pediatric patients. Aims: To describe clinical and echo features of MR in NCCM. Methods: All pediatric patients with NCCM associated with MR and preserved ventricle function seen in one center from January 2015 to March 2020 were included. Clinical and echo features were described. Results: Twelve patients were identified (66% females), 8 (66%) presented with heart failure due to severe MR , and 4 were asymptomatic with mild-moderate MR. Echo features in all patients showed Papillary Muscle Noncompaction (PMNC). The Papi... view moreĀ»