Journal of Spine & NeurosurgeryISSN: 2325-9701

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Research Article, J Spine Neurosurg Vol: 5 Issue: 5

Management of Syringohydromyelia Associated with Basilar Impression and Osteogenesis Imperfecta

Orakcioglu B*, Aschoff A and Unterberg A
Neurochirurgische Klinik und Poliklinik, Ruprecht-Karls-Universität, Im Neuenheimer Feld 400, D-69120 Heidelberg, Germany
Corresponding author : Dr. Berk Orakcioglu
Neurochirurgische Klinik und Poliklinik, Ruprecht-Karls-Universität, Im Neuenheimer Feld 400, D-69120 Heidelberg, Germany
Tel: +49 6221 5638922
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E-mail: [email protected]
Received: January 06, 2016 Accepted: June 04, 2016 Published: June 11, 2016
Citation: Orakcioglu B, Aschoff A, Unterberg A (2016) Management of Syringohydromyelia Associated with Basilar Impression and Osteogenesis Imperfecta. J Spine Neurosurg 5:5. doi: 10.4172/2325-9701.1000236

Abstract

Objective: Syringomyelia associated with osteogenesis imperfecta and basilar impression is a rarely seen pathology. We herein report our management experiences of patients with this rare condition. Methods: We overlook 4 patients with osteogenesis imperfecta, basilar impression and syringohydromyelia. All patients were symptomatic at presentation. One patient received a syringosubarachnoid shunt at the craniocervical junction and 2 patients underwent cranio-cervical decompression with duraplasty. One patient was followed conservatively. Follow up periods of these patients ranged up to 14 years. Results: Two patients that received a cranio-cervical decompression showed complete remission of clinical symptoms through the followup period. One patient who was treated by a syringo-subarachnoid microcatheter shunt had early regression of spinal cord symptoms, but died 6 weeks after surgery. One conservatively treated patient remained neurologically unchanged and therefore surgery was not advocated. Conclusions: Cranio-cervical decompression and duraplasty is a treatment option for symptomatic patients with syringohydromyelia and basilar impression accompanying osteogenesis imperfecta resulting in acceptable perioperative morbidity.

Keywords: Syringomyelia; Osteogenesis imperfecta; Cranio-cervical decompression; Duraplasty

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