Journal of Spine & NeurosurgeryISSN: 2325-9701

Reach Us +1 850 754 6199
All submissions of the EM system will be redirected to Online Manuscript Submission System. Authors are requested to submit articles directly to Online Manuscript Submission System of respective journal.

Management of Syringohydromyelia Associated with Basilar Impression and Osteogenesis Imperfecta

Objective: Syringomyelia associated with osteogenesis imperfecta and basilar impression is a rarely seen pathology. We herein report our management experiences of patients with this rare condition. Methods: We overlook 4 patients with osteogenesis imperfecta, basilar impression and syringohydromyelia. All patients were symptomatic at presentation. One patient received a syringosubarachnoid shunt at the craniocervical junction and 2 patients underwent cranio-cervical decompression with duraplasty. One patient was followed conservatively. Follow up periods of these patients ranged up to 14 years. Results: Two patients that received a cranio-cervical decompression showed complete remission of clinical symptoms through the followup period. One patient who was treated by a syringo-subarachnoid microcatheter shunt had early regression of spinal cord symptoms, but died 6 weeks after surgery. One conservatively treated patient remained neurologically unchanged and therefore surgery was not advocated. Conclusions: Cranio-cervical decompression and duraplasty is a treatment option for symptomatic patients with syringohydromyelia and basilar impression accompanying osteogenesis imperfecta resulting in acceptable perioperative morbidity.

Special Features

Full Text

View

Track Your Manuscript

Share This Page

Media Partners

Associations