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Aggressive Intrathecal Adult Granulosa Cell Tumor Causing Cauda Equina Syndrome | SciTechnol

Clinical Oncology: Case Reports.

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Case Report, Clin Oncol Case Rep Vol: 4 Issue: 2

Aggressive Intrathecal Adult Granulosa Cell Tumor Causing Cauda Equina Syndrome

Razia Rehmani1* and Oscar Cisneros2

1Department of Radiology, Chief of Neuroradiology, Saint Barnabas Health Care System, Albert Einstein University Hospital, New York

2Department of Internal Medicine, Internal Medicine, Saint Barnabas Health Care System, Albert Einstein University Hospital, New York

*Corresponding Author:Razia Rehmani
Department of Radiology, Chief of Neuroradiology
Saint Barnabas Health Care System
Albert Einstein University Hospital, New York
E-mail: rrehmani@sbhny.org

Received: September 14, 2020 Accepted: December 25, 2020 Published: February 10, 2021

Citation:Rehmani R, Cisneros O (2021) Aggressive Intrathecal Adult Granulosa Cell Tumor Causing Cauda Equina Syndrome. Clin Oncol Case Rep 4:2

Abstract

Abstract

Granulosa Cell Tumor (GCT) are the most common malignant sex cord stromal tumors and contain both sex cord and stromal components. They account for approximately 3%-5% of all ovarian tumors. GCT are slow growing indolent tumors with a favorable prognosis. However recurrence is associated with high mortality. Metastasis is rare, they present with nonspecific symptoms of abdominal bloating and distention as well as symptoms due to hormonal imbalance due to estrogenic activity of the tumor. There are two classifications of GCT which include Juvenile and adult variants. High recurrence rate is a major factor responsible for mortality associated with these tumors. We report a case of locally aggressive GCT of the abdomen with infiltration into the bony lumbar vertebrae before invading the entire spinal canal resulting in cauda equina syndrome. To our knowledge such an extensive locally aggressive GCT with adjacent bony and intrathecal extension from the abdomen into the thecal sac has not been reported. Given the indolent course of this disease, early diagnosis and treatment are critically important for best outcome.

Keywords: Adult granulosa cell tumor; Juvenile granulosa cell tumor; Metastais; Stromal tumors; FOXL2 mutation; Late recurrence

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